Biochemistry · USMLE Step 1

USMLE Biochemistry: Vitamins and Cofactors

Fat- and water-soluble vitamins, cofactors, and their deficiency syndromes tested on USMLE Step 1.

35 cards · basic cards · AI-written, checked twice. Edit anything.

Study this set free Get FlashKeepers for iPhone
Which vitamin deficiency classically causes night blindness (nyctalopia)?
Vitamin A
What is the active form of vitamin A found in the retina that combines with opsin to form rhodopsin?
11-cis-retinal
Chronic vitamin A toxicity can cause which type of intracranial condition?
Pseudotumor cerebri (idiopathic intracranial hypertension)
Thiamine (vitamin B1)
Thiamine pyrophosphate (TPP), its active coenzyme form
Name the four enzymes for which thiamine pyrophosphate (TPP) is a required cofactor.
Pyruvate dehydrogenase, alpha-ketoglutarate dehydrogenase, transketolase, and branched-chain ketoacid dehydrogenase
In Wernicke encephalopathy, thiamine deficiency classically causes a triad of confusion, ophthalmoplegia, and ____.
ataxia
What are the hallmark features of Korsakoff syndrome?
Confabulation and anterograde/retrograde memory loss
Wet beriberi primarily affects which organ system, and dry beriberi affects which?
Wet beriberi affects the cardiovascular system (high-output heart failure); dry beriberi affects the nervous system (peripheral neuropathy)
Why should thiamine be given before glucose in a malnourished or alcoholic patient?
Glucose infusion can precipitate acute Wernicke encephalopathy by depleting remaining thiamine stores
What are the two active coenzyme forms of riboflavin (vitamin B2)?
FAD and FMN
What are two classic signs of riboflavin (B2) deficiency?
Cheilosis (cracking at mouth corners) and corneal vascularization
What are the two active coenzyme forms of niacin (vitamin B3)?
NAD+ and NADP+
Niacin can be endogenously synthesized from which essential amino acid?
Tryptophan
Pellagra, caused by niacin deficiency, presents with the classic triad of diarrhea, dermatitis, and ____.
dementia
Hartnup disease impairs intestinal and renal absorption of which class of amino acids, leading to pellagra-like symptoms?
Neutral amino acids (including tryptophan)

20 more cards in the app